PAPILLARY CRANIOPHARYNGIOMA

PAPILLARY CRANIOPHARYNGIOMA
  • It is a well differentiated pseudopapillary neoplasm of the suprasellar  and sellar regions
  • other term used is suprasellar papillary squamous epithelioma
  • The origin of this lesion is unknown but suggested possibility is from Rathke cleft cyst.
  • Clinical features
    • unlike classical adamantinomas, papillary craniopharyngioma as usually occur in adults
    • These tumors may have affect on the visual system, CSF flow, personality and mental capacity
  • Site: 
    • Lesions are commonly suprasellar than intrasellar
    • Many tumors occur with in third ventricle
  • Gross 
    • Lesions may be solid or cystic or a cyst with small papillary nodule
    • Calcifications are rarely seen
  • Microscopic findings
    • Tumor is composed of sheets of well differentiated squamous cells separated by prominent cores of fibrovascular stroma
    • Cellular sheets dehisce to create prominent pseudopapillae
    • Small epithelial whorls may be present
    • Palisading basal cell layer may not be prominent
    • Stellate reticulum is usually absent
    • Goblet cells and ciliated cells may be focally present
    • Calcifications are usually absent
  • Immunohistochemistry
    • Positive for – Cytokeratins, EMA, CK-7 (Superficial and non-basal layer)
    • Negative for– CK-8, and CK 20.
  • Treatment – surgical resection
Reference
  • Peter C. Burger, Bernd W. Scheithauer. Craniopharyngiomas. In: Tumors of the central nervous system. AFIP Atlas of tumor pathology Series 4. Chapter 15. 461-470